#Ernemannturm

Eines jener klassischen Motive, das ich immer wieder mit unterschiedlichen Linsen/Kameras ablichte. Dieses Mal mit der #Alpha7Rm2 und dem relativ weitwinkeligen #Meike35mmF2, von der Rückseite, mit etwas mehr Kontext vom restlichen Gebäude.

#ernemannwerke #technischeSammlungen #tsd #dresden #nofilter #pentacon #Striesen

Acabo de subir este episodete, que llevaba retrasito.
TSD T2 E4 | Bueno es tener amigos aunque sea en el infierno

https://episodes.fm/aHR0cHM6Ly9mZWVkcy5hY2FzdC5jb20vcHVibGljL3Nob3dzLzY1YjdiNjk4MjNiOGRjMDAxNjVjZjhlMQ/episode/Njg2ZWJmN2I4ZDNkNjgzOWY0MWVhNjI3

A través de ese enlace podéis elegir desde donde escucharlo y suscribiros si os gustan nuestras majaderías.
Estamos pasando unas semanas bastante difíciles por lo que hemos tenido que pararlo todo en seco. Con suerte podremos volver a empujar esto pronto, que ganas no nos faltan. 🤞

#TSD #TodoSonDesgracias #podcast #espanol

TSD T2 E4 | Bueno es tener amigos aunque sea en el infierno

Listen to TSD T2 E4 | Bueno es tener amigos aunque sea en el infierno from Todo Son Desgracias wherever you get your podcasts!

¿Estás pensando en opositar al Departamento de Justicia? ¡Conviértete en un héroe en el Departamento del Sheriff!

Y aunque no sea así, puedes descubrir todo acerca de la Traffic Services Detail si acudes hoy a Legion Square, en Los Santos.

Son mucho más que una división de tráfico, son héroes cotidianos que velan por nuestra seguridad en cada esquina, asegurando que nuestras calles sean más seguras para todos.

#LSSD #aTraditionOfService #tsd #XXXVIAcademiaDoJ

Targeted Sequencing of HEXA Gene Shows Missense Substitution (p.Arg499His) in a Large Pakistani Family with Tay-Sachs Disease - #HEXA #HEXB #TSD #GM2gangliosidosis #βNacetylhexosaminidaseA #Pakistan - https://link.springer.com/article/10.3103/S0095452724050025
Targeted Sequencing of HEXA Gene Shows Missense Substitution (p.Arg499His) in a Large Pakistani Family with Tay-Sachs Disease - Cytology and Genetics

Abstract Tay-Sachs disease or GM2 gangliosidosis, is caused by a deficiency of beta-hexosaminidase A (HEXA), resulting in lysosomal accumulation of GM2 ganglioside. However, deficiencies or reduced activities of HEXA and HEXB result in Sandhoff disease. The patients manifest with the macular cherry-red spots due to lipid-laden ganglion cells, hypotonia, low muscle tone, intractable seizures, developmental arrest, blindness, and neurological deterioration. The aim of this study was to identify the TSD-causing variant in a large Pakistani family showing typical symptoms of Tay-Sachs disease. Here, we studied a large Pakistani family with six TSD patients for the identification of the pathogenic variant by targeted DNA sequencing. As a result, we identified a missense substitution (p.Arg499His) in exon 13 of HEXA that was completely cosegregated among affected and normal individuals. In conclusion, we identified a missense substitution (p.Arg499His) in HEXA gene in a large consanguineous Pakistani family and further enriched the mutational spectrum of HEXA through Pakistani patients for the early diagnosis of the disease.

SpringerLink

दिल्ली में बदला सियासी पारा! भाजपा ने खेला दांव #delhielection #arvindkejriwal #rahulgandhi #modi

दिल्ली में बदला सियासी पारा! भाजपा का खेल शुरू ? #delhielection #arvindkejriwal #rahulgandhi #modi दिल्ली विधानसभा चुनाव में बदल रहा है सियासी खेल । भाजपा ने खेला अपना दांव । बदल रही है दिल्ली की राजनीति । The Social Dice दिल्ली के झुग्गियों का असली सच | #delhislums #arvindkejriwal #congress #bjp #tsd Exclusive Ground Report | #delhislums #mumbaislum #dharavi

https://spinelessnews.com/%e0%a4%a6%e0%a4%bf%e0%a4%b2%e0%a5%8d%e0%a4%b2%e0%a5%80-%e0%a4%ae%e0%a5%87%e0%a4%82-%e0%a4%ac%e0%a4%a6%e0%a4%b2%e0%a4%be-%e0%a4%b8%e0%a4%bf%e0%a4%af%e0%a4%be%e0%a4%b8%e0%a5%80-%e0%a4%aa%e0%a4%be/

दिल्ली में बदला सियासी पारा! भाजपा ने खेला दांव #delhielection #arvindkejriwal #rahulgandhi #modi - Spineless News Channels

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Spineless News Channels
क्या #अखिलेशयादव करेंगे "महाकुम्भ" में स्नान ? #tsd #akhileshyadav #akhileshvsyogi #yogiadityanath - Spineless News Channels

क्या #अखिलेशयादव करेंगे "महाकुम्भ" में स्नान ? #tsd #news #rajpalyadav #akhileshyadav #akhileshvsyogi #yogiadityanath #omprakashrajbhar #lotan #lordhanuman

Spineless News Channels
मोदी जी के शासन में रेलवे की स्थिति सुपरफास्ट हो गई ? #tsd #news #pmmodi #bjp #indianrailways - Spineless News Channels

मोदी जी के शासन में रेलवे की स्थिति सुपरफास्ट हो गई ? #tsd #news #pmmodi #bjp #indianrailways #railway #bjpnews #bjpleader #educationsystem #population

Spineless News Channels
आजमगढ़ को मिली नई परियोजनाए ? #tsd #news #dharmendrayadav #azamgarhnews #azamgarh #the_social_dice - Spineless News Channels

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युवा ने सीएम नीतीश कुमार को गाली क्यों दी ? #tsd #news #nitishkumar #biharcmnitish #biharnewstoday - Spineless News Channels

युवा ने सीएम नीतीश कुमार को गाली क्यों दी ? #tsd #news #nitishkumar #biharcmnitish #biharnews #biharnewstoday #kejrival #delhielection #delhichunav

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बुजुर्ग महिला ने किया केजरीवाल को फोन ? #tsd #news #kejrival #delhielection #arvindkejriwal #delhicm - Spineless News Channels

बुजुर्ग महिला ने किया केजरीवाल को फोन ? #tsd #news #kejrival #delhielection #delhichunav #delhielection2025#delhislums #mumbaislum

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